Maple syrup urine disease is a genetic disorder where a person cannot process certain proteins. Smell the toddler's breath, if it, too, smells sickly sweet like maple syrup, go to the doctor. It is unusual for a healthy female on medicines to suddenly develop a body odor like maple syrup. The condition is named for the sweet odor of the urine of untreated babies. This leads to a buildup of these chemicals in the blood. sweetypuffs. Now, when do weird or bad baby smells indicate a problem? There are many instances when a weird or bad baby smell may indicate a health problem. This may not always be present in all types. so I figured, if he can smell it too I'm going to look it up online. Answer 1 of 19: So, I'm at my local bank today and the teller asks about my upcoming Canadian vacation. Sometimes there is increased discharge. I googled and I don't think I have maple syrup urine disease, especially since it's not my urine that smellsâ¦ We live in a block of 4 town homes so thought, although weird maybe someone just made pancakes. These amino acids and their toxic byproducts build up in the blood and urine, resulting in symptoms such as lethargy, poor appetite, seizures, and vomiting. These rare disorders are trimethylaminuria, maple syrup urine disease etc. Infants with this type of maple syrup urine disease will show symptoms within the first several days of life. My 2 year old has had this 'syrupy' sweet smell for about 6ish months now. She asks if I need currency and I explain that I don't as I usually use my travel credit card instead. She has a dry diaper so its not that. Our 8 y/o daughter has very occasionally had breath that smells like maple syrup. All of my children have had this smell as toddlers and Ive always wondered why! Itâs when he wears his fleece ones to bed (clean) and by morning I can smell it on them. Charlie: Yeah. I'm a 41 year old female and on several occasions in the past six months, I've noticed that I smell really sweet, almost a maple syrupy smell. Frequent shower does no good. what will cause your sweat/body odor to smell like maple syrup? Her urine smells normal - no sweet smell; her perspiration is not abnormal either. The genetic defect is so named after its tell-tale symptom of characteristic, sweet smeling body secretions like urine, sweat, and earwax that is oddly reminiscent of maple syrup. He never wants to eat and when he does eat, it's 2 or 3 bites and then he says he's full. Poor feeding, vomiting, loss of appetite, irritability. It means the body cannot process certain amino acids (the "building blocks" of protein), causing a harmful build-up of substances in the blood and urine. It's happened about 3 or 4 times over the past year, as clearly as we can figure. It smells like maple-syrup. See detailed information below for a list of 1 causes of Maple syrup smelling urine in children, including diseases and drug side effect causes. Babies with the disease feed poorly, vomit, and have seizures and occasionally brain swelling. According to his dr., he's 10% in height & weight on the growth charts. It's hard to work out in public places because of this. Normally, our bodies break down protein foods such as â¦ Page 1 of 3 1 2 3 Next > ghostonvacation Well-Known Member. Typically the odor is fishy, but odor is very subjective and one person's "maple syrup" may be another's "fishy". : i woke up to baby crying at 2am and i noticed her diaper smelled very sweet, almost like maple syrup. Some dogs smell like corn chips, nachos and sometimes like body powder. I thought for a couple days that she was stinky but disregarded it. It is an inherited disorder , and a parent may notice their baby or child has sweet-smelling urine. However, there is a common condition that results in sweet breath: Canine Diabetes. Some dog owners show a lot of concern when their dog smells like maple syrup. A Verified Doctor answered. Feb 25th '12. When I sweat my body odor smells like onions. MSUD is considered an amino acid condition because people with MSUD have trouble breaking down certain amino acids, the building blocks of proteins. Feb 25th '12. This is a very weird smell for dogs and it stays on even if you thoroughly bath your dog applying some shampoos with fragrance as well. The type of Freon is R410A some say it a leak. » Review Causes of Maple syrup smelling urine in children: Causes Sluggish/slow/tiredness and weakness. People with this condition cannot break down the amino acids leucine, isoleucine, and valine. Also, for the last year or so, he has lost 3 lbs. my apartment smells like maple syrup. One morning I made my DH sniff it and he was like "smells like that fenugreek stuff you used to take." Why does my child smell like maple syrup? Absolutely, but as far as that goes, Iâd investigate the walls. The condition gets its name from the distinctive sweet odor of affected infants' urine, particularly prior to diagnosis and during times of acute illness. A few days ago the wife and I came home and could smell a super sweet smell that reminded of us maple syrup. I'm hoping it's neither! Help! Any idea what could cause this? Discussion in 'The Toddler Years(1-3)' started by i4get, May 29, 2008. i4get Well-Known Member. Like in humans, Canine Diabetes is a serious condition. I've read about maple syrup urine disease or could be a sign of diabetes. The disease prevents your body from breaking down certain amino acids. It causes an inability for the body to break down the amino acids valine, leucine and isoleucine. Holly. instead of gaining any weight. Maple syrup urine disease (MSUD) is a rare but serious inherited condition. This is rare but is seen in some metabolic disorders. Maple syrup urine disease (MSUD) is an inherited condition caused by a faulty gene. Classic maple syrup urine disease is the most common type. She asks if I need currency and I explain that I don't as I usually use my travel credit card instead. She is almost 7 weeks old and this is the first time I noticed this. Trichomonas causes similar odor, and other STDs like gonorrhea or chlamydia are more common in BV. Maple syrup smelling urine in children: Introduction. 1 doctor answer. This causes a build-up of harmful levels of these substances in the blood. My toddler smelling like syrup? Add Friend Ignore [a k&m] 2 kids; Iowa 6968 posts. See a doctor soon to check it out. A child can recover if diagnosed early and treated appropriately. Maple syrup urine disease (MSUD) is inherited, which means it is passed down through families. If he is taking a lot of whey protein powder, he's getting a lot of branched-chain amino acids, and they have an odor of maple syrup. Of course I just googled it and there's tons of info about Maple Syrup Urine Disease (which is very bad news if that's what it is). I donât know why something would smell like maple syrup in a house that is constructed like it is. Do you mysteriously smell maple syrup everywhere? It still smells like maple syrup. I've noticed a couple of nights that Morgan smells like maple syrup. Want to know more about maple syrup urine disease and its symptoms? But being tired all the time is certainly a symptom of diabetes. So I google and find "maple syrup urine disease" and think THAT'S IT! A US doctor answered Learn more. Charlie: Well, itâs the bedroom-Tom: Those smell questions are tough. In children with MSUD, the body cannot break down certain amino acids, the building blocks of protein. He actually still smells like that when his blood sugar is high. A scent of maple syrup may mean maple syrup urine disease a genetic disorder. Maple syrup smell: Okay this sounds strange Iâm sure but for a while Iâve noticed my sonâs pjâs smell like maple syrup in the mornings. Changes in muscle tone â poor muscle tone, muscle tightness/tension I know thereâs a newborn condition that causes urine to smell like that but Iâm sure we would have known if he had that by now! urine that smells like maple syrup or burnt sugar; Babies with MSUD have episodes of illness called metabolic crisis This is a serious health condition caused by low blood sugar and the build-up of toxic substances in the blood. The bedroom, the closet and the bathroom, so â¦ For example, a musty odor can mean a rare but serious condition called Phenylketonuria. Urine, sweat, or earwax that smells like maple syrup or burnt sugar. Baby's pee smelled like maple syrup? But it has persisted for a few days. Rachel had maple syrup urine disease. Overview. [a k&m] 2 kids; Iowa 6968 posts . It seems to last all day, and to be coming from my skin! It is managed through diet with severe protein restriction. Answer 11 of 19: So, I'm at my local bank today and the teller asks about my upcoming Canadian vacation. Maple syrup urine disease is an extremely rare genetic disorder in a healthy individual certain enzymes breakdown amino acids found in protein-rich foods, but in patients like Rachel, those enzymes are absent, allowing the amino acids to wreak havoc on the brain. I know it sounds weird, but my initial reaction to reading that was "oh, diabetes". 1 decade ago. It is still blowing cold air. I have let this machine run for hours . and we both said "like maple syrup." Maple syrup: Maple syrup urine disease occurs when the body can't process certain amino acids. Individuals with classic maple syrup urine disease have little or no enzyme activity (usually less than 2 % of normal). Maple syrup urine disease (MSUD) is a metabolic disorder that is genetically inherited 2. Maple syrup urine disease (MSUD) is a condition in which the body is unable to break down certain proteins. 2 0. You probably donât have maple syrup urine disease because itâs a rare inherited disorder that affects an estimated 1 in 185,000 infants worldwide, according to the National Institutes of Health. My Dogâs Breath Smells Like Maple Syrup. Toddler Urine Smells Like Maple Syrup. It doesn't always happen but now and then my daughter's pee smells really sweet, like maple syrup. He weighs 32 lbs. (This disorder got its name from this common symptom.) Maple syrup urine disease (MSUD) is an autosomal recessive metabolic disorder affecting branched-chain amino acids.It is one type of organic acidemia. ... obviously they found a portal that leads them to a maple syrup pool and they swim in it, get a giant pancake to float on, and so on. Dogsâ breath often smells funky, and a particularly bad stink can indicate serious illnesses like kidney disease and liver problems. Maple syrup smelling urine in children: Maple syrup smelling urine in children refers to a child's urine that smells like maple syrup. Posted 03/11/2011. It is caused by a defect in 1 of 3 genes. Maple syrup urine disease (MSUD) is a rare, inherited metabolic disorder. Joined: Jan 16, 2012 Messages: 9,368 Likes Received: 12,524 #1 ghostonvacation, Sep 15, 2012. Discussion in 'General' started by ghostonvacation, Sep 15, 2012. !